97久久久精品综合88久久_亚洲国产精品一_久热热国产久热_97操操操_北条麻妃在线免费观看_精品国自产拍天天拍

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
99久久精品一区二区三区,91香蕉视频免费版,午夜精品福利一区二区三区蜜桃
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-Myelin PLP/RBITC Conjugated antibody (bs-11093R-RBITC)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-11093R-RBITC
英文名稱 Rabbit Anti-Myelin PLP/RBITC Conjugated antibody
中文名稱 羅丹明(RBITC)標記的髓磷酯髓鞘蛋白1抗體
別    名 Lipophilin; HLD1; Lipophilin; Major myelin proteolipid; Major myelin proteolipid protein; MMPL; Myelin proteolipid protein; MYPR_HUMAN; PLP 1; PLP; PLP/DM20; PLP1; PLP1 protein; PMD; Proteolipid protein 1 (Pelizaeus Merzbacher disease spastic paraplegia 2 uncomplicated); myelin proteolipid protein or lipophilin; Proteolipid protein 1; SPG 2; SPG2.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 神經生物學  細胞粘附分子  細胞膜蛋白  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Dog, Cow, Horse, Rabbit, Monkey, )
產品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 30kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human Myelin proteolipid protein
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
PLP is a major constituent of myelin. The two isoforms of the myelin proteolipid protein, PLP and DM20, are very hydrophobic integral membrane proteins that account for about half of the protein content of adult CNS myelin. A mutation in the gene which encodes PLP is linked to Pelizaeus-Merzbacher disease (PMD), a chronic infantile type of diffuse cerebral sclerosis. The gene which encodes PLP maps to human chromosome Xq22. The glycoprotein zero (also designated P-zero or myelin peripheral protein) is the primary structural protein of peripheral myelin, and accounts for more than 50% of the protein present in the peripheral nerve sheath. Zero is an integral membrane glycoprotein. Expression of zero is restricted to Schwann cells. The gene which encodes zero maps to human chromosome 1q22. PMP22 (peripheral myelin protein 22) is a growth-regulated membrane protein which is expressed by Schwann cells and is localized primarily in compact peripheral nervous system myelin. The gene which encodes PMP22 maps to human chromosome 17p11.2.

Function:
This is the major myelin protein from the central nervous system. It plays an important role in the formation or maintenance of the multilamellar structure of myelin.

Subunit:
Belongs to the myelin proteolipid protein family.

Subcellular Location:
Membrane; Multi-pass membrane protein.

DISEASE:
Defects in PLP1 are the cause of leukodystrophy hypomyelinating type 1 (HLD1) [MIM:312080]; also known as Pelizaeus-Merzbacher disease. HLD1 is an X-linked recessive dysmyelinating disorder of the central nervous system in which myelin is not formed properly. It is characterized clinically by nystagmus, spastic quadriplegia, ataxia, and developmental delay.
Defects in PLP1 are the cause of spastic paraplegia X-linked type 2 (SPG2) [MIM:312920]. SPG2 is characterized by spastic gait and hyperreflexia. In some patients, complicating features include nystagmus, dysarthria, sensory disturbance, mental retardation, optic atrophy.

Similarity:
Belongs to the myelin proteolipid protein family.

Database links:

Entrez Gene: 281410 Cow

Entrez Gene: 481002 Dog

Entrez Gene: 5354 Human

Entrez Gene: 18823 Mouse

Entrez Gene: 24943 Rat

Omim: 300401 Human

SwissProt: P04116 Cow

SwissProt: P23294 Dog

SwissProt: P60201 Human

SwissProt: P60202 Mouse

SwissProt: P60203 Rat

Unigene: 49691 Cow

Unigene: 1787 Human

Unigene: 1268 Mouse

Unigene: 4550 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.kastlife.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 国产精品影视在线 | 二区三区偷拍浴室洗澡视频 | 欧美性猛交视频 | 国产精品午夜爆乳美女 | 午夜精品一区二区三区福利视频 | 久久无毛 | 日本精品中文字幕在线不卡 | 欧美精品免费观看二区 | 91老司机福利在线视频 | 97在线观看免费版高清 | 北条麻妃中文字幕 | 中文字幕一区二区三区av | 亚洲精品456在线播放第一页 | 久草在线小说 | 日韩网站一区二区 | 国产毛片精品 | 十八禁视频网站在线观看 | 亚洲欧美闷骚少妇影院 | 久久综合操 | 2020久久超碰国产精品最新 | 久久国产禁久久 | 六十路高龄老熟女m | 国内一级黄色大片 | 综合自拍亚洲综合图区高清 | 男男GAY亚洲帅哥在线 | 国产精品久久久久久AV福利 | 欧美性xxxx视频 | 不戴奶罩的教师水卜樱在线观看 | 国产三级专区精品 | 国内精品免费久久久久软件 | 亚洲国产精品成人av | 日日爱69| 久久热这里只有精品在线观看 | 99激情网 | 中文字幕在线观看不卡视频 | 国产精品无码一区二区三区无卡 | 国产精品天美传媒沈樵 | 日韩欧精品无码三级片 | 精品一区日韩成人 | 伊甸园永久入口www 加勒比HEZYO无码专区 | 国产一级淫片a按摩推澡按摩 |