97久久久精品综合88久久_亚洲国产精品一_久热热国产久热_97操操操_北条麻妃在线免费观看_精品国自产拍天天拍

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
中文字幕亚洲第一,精品国产无套在线观看,亚洲日韩一区二区三区
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-FECH/PE-Cy3 Conjugated antibody (bs-9521R-PE-Cy3)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-9521R-PE-Cy3
英文名稱 Rabbit Anti-FECH/PE-Cy3 Conjugated antibody
中文名稱 PE-Cy3標記的鐵螯合酶抗體
別    名 EPP; FCE; Ferrochelatase (protoporphyria); Ferrochelatase; Ferrochelatase mitochondrial; Heme synthetase; Protoheme ferro lyase; HEMH_HUMAN.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 心血管  細胞生物  免疫學  細胞類型標志物  細胞骨架  線粒體  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Sheep, )
產品應用 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 43kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human EPB41
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
Ferrochelatase catalyzes the insertion of the ferrous form of iron into protoporphyrin IX in the heme synthesis pathway, and is localised in the mitochondrion. Defects in ferrochelatase are associated with protoporphyria. Two transcript variants encoding different isoforms have been found for this gene. Porphyrias are a group of inherited or acquired disorders of certain enzymes in the heme biosynthetic pathway (also called porphyrin pathway). They are broadly classified as hepatic porphyrias or erythropoietic porphyrias, based on the site of the overproduction and mainly accumulation of the porphyrins (or their chemical precursors). They manifest with either skin problems, or neurological complications, or occasionally both.

Function:
Catalyzes the ferrous insertion into protoporphyrin IX.

Subunit:
Homodimer.

Subcellular Location:
Mitochondrion inner membrane; Peripheral membrane protein; Matrix side.

DISEASE:
Defects in FECH are the cause of erythropoietic protoporphyria (EPP) [MIM:177000]. Porphyrias are inherited defects in the biosynthesis of heme, resulting in the accumulation and increased excretion of porphyrins or porphyrin precursors. They are classified as erythropoietic or hepatic, depending on whether the enzyme deficiency occurs in red blood cells or in the liver. EPP is a form of porphyria marked by excessive protoporphyrin in erythrocytes, plasma, liver and feces, and by widely varying photosensitive skin changes ranging from a burning or pruritic sensation to erythema, edema and wheals.

Similarity:
Belongs to the ferrochelatase family.

Database links:

Entrez Gene: 2235 Human

Omim: 612386 Human

SwissProt: P22830 Human

Unigene: 365365 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.kastlife.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 亚洲欧美国产日韩精品 | 少妇大胆瓣开下部自慰 | 天地争霸美猴王国语在线观看免费 | 欧美黄色一级片视频 | 唐人街探案网剧免费观看 | 久久大香伊蕉在人线免费 | 狠狠色视频 | 国产精品r级最新在线观看 一区三区在线观看 | 日韩欧美亚洲国产精品字幕久久久 | 国产成人精品一区一区一区 | 97精品人人A片免费看 | 国产AV国片精品有毛 | 伊人综合久久 | 狠狠躁夜夜躁人人躁婷婷视频 | jvid视频在线观看免费 | 欧美人与动牲交免费观看网 | 中日精品一色哟哟 | 欧美成人看片一区二区三区尤物 | 国产欧美一区二区精品三级 | 亚洲国产一成久久精品 | 97精品视频在线观看自产线路二 | 国产AV无码精品国产精品 | 乱码一区二区三区四区 | 激情综合网五月激情 | 在线观看日本一区 | 日本黄色五级片 | 加勒比无码一区二区三区 | 国产高清福利无码视频 | 免费在线观看一区二区三区 | 欧美日韩精品一区二区三区高清视频 | 神马久久久久久久久久久 | 中文字幕免费精品一区高清 | 国产欧美日韩在线观看一区二区 | 又粗又黄又硬又爽的免费视频 | 亚洲日本va午夜中文字幕久久 | 91看点 | 国产在线观看无码一区二区三区 | 激烈18禁高潮视频免费 | 青青草小视频 | 宅男66LU国产在线观看 | 国产二级一片内射视频播放 |