97久久久精品综合88久久_亚洲国产精品一_久热热国产久热_97操操操_北条麻妃在线免费观看_精品国自产拍天天拍

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
欧美一区二区在线视频,伊人久久综合精品一区二区三区,免费看片国产
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-FAM20C/FITC Conjugated antibody (bs-12376R-FITC)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-12376R-FITC
英文名稱 Rabbit Anti-FAM20C/FITC Conjugated antibody
中文名稱 FITC標記的胞外分泌型絲氨酸/蘇氨酸蛋白激酶FAM20C抗體
別    名 C76981; Dentin matrix protein 4; DKFZp547C074; DMP-4; DMP4; DMP4_HUMAN; Extracellular serine/threonine protein kinase Fam20C; Fam20c; Family with sequence similarity 20 member C; GEF CK; Golgi enriched fraction casein kinase; Protein FAM20C; RNS antibod.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 細胞生物  發育生物學  信號轉導  干細胞  激酶和磷酸酶  細胞外基質  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 Rat,  (predicted: Human, Mouse, Chicken, Dog, Cow, Horse, Sheep, Monkey, )
產品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 64kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human FAM20C
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
The FAM20 proteins are a family of secreted proteins that regulate differentiation and function of hematopoietic and other tissues. FAM20C, also known as DMP4 (Dentin matrix protein 4), is a 570 amino acid secreted protein that binds calcium and may play a role in dentin mineralization. Defects in the gene encoding FAM20C are the cause of Raine syndrome (Lethal osteosclerotic bone dysplasia), an autosomal recessive osteosclerotic bone dysplasia, that is characterized by generalized osteosclerosis, microencephaly and craniofacial dysplasia. Usually, affected individuals survive only days or weeks. The mutations of the FAM20C gene include four nonsynomous base changes and four splice-site changes that have a detrimental affect on splicing.

Function:
Calcium-binding protein which may play a role in dentin mineralization.

Subcellular Location:
Secreted.

Tissue Specificity:
Widely expressed.

DISEASE:
Defects in FAM20C are the cause of Raine syndrome (RNS) [MIM:259775]. RNS is an autosomal recessive osteosclerotic bone dysplasia with neonatal lethal outcome. Clinical features include generalized osteosclerosis, craniofacial dysplasia and microcephaly.

Similarity:
Belongs to the FAM20 family.

Database links:
UniProtKB/Swiss-Prot: Q8IXL6.2

Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.kastlife.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 欧美生活1级| 在线播放视频 | 99R在线精品视频在线播放 | 美女黄色网址 | 中文字幕免费在线视频 | 黄色片免费观看网站 | 影音先锋男人站 | 久久国产亚洲日韩 | 噜噜噜在线观看免费视频日本 | av久久伊人精品中文字幕 | 国产综合色在线视频 | 国语自产拍在线视频中文 | 国产精品久久久久久久久久了 | 亚洲欧美日韩精品久久 | 免费网站看V片在线18禁无码 | 白虎视频污| 91天堂| 久久精品国产亚洲A∨麻豆 日本在线看片免费人成视频 | 日韩精品国产自在久久现线拍 | 国产AV永久无码精品网站 | 日韩1级| 亚洲女同成av人片在线观看 | 国产香蕉视频在线 | 欧美精品乱码久久久久久 | 56精品视频在线播放免费观看 | 亚洲AV无码一区二区三区观看 | 麻豆人妻少妇精品无码专区 | 精品国产第一福利网站 | 精品人妻无码一区二区三区丝袜 | 啪啪免费看 | 91大神视频在线免费观看 | 五月丁香综合激情六月久久 | 国产精品无码免费视频二三区 | 邻居少妇张开腿让我爽了在线观看 | 一级黄色片免费看 | 亚洲富人天堂视频 | 大地资源在线观看免费高清一 | 蜜臀色欲AV无码国产精品 | 无码精品人妻一区二区三区涩爱 | 久久九九免费视频 | 简单av自拍 |