97久久久精品综合88久久_亚洲国产精品一_久热热国产久热_97操操操_北条麻妃在线免费观看_精品国自产拍天天拍

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
国产精品亚洲三区,日韩极品一区,亚洲婷婷一区二区三区
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-GLDC/BF594 Conjugated antibody (bs-13370R-BF594)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-13370R-BF594
英文名稱 Rabbit Anti-GLDC/BF594 Conjugated antibody
中文名稱 BF594標記的甘氨酸脫羧酶P蛋白抗體
別    名 GCE; GCSP; GCSP_HUMAN; GLDC; Glycine cleavage system P protein; glycine cleavage system protein P; Glycine decarboxylase; glycine decarboxylase P protein; Glycine dehydrogenase (decarboxylating) mitochondrial; Glycine dehydrogenase [decarboxylating], mitochondrial; Gycine dehydrogenase (decarboxylating); HYGN1; MGC138198; MGC138200; NKH.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 腫瘤  細胞生物  信號轉導  激酶和磷酸酶  新陳代謝  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應
產品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 109kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human GLDC
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
The glycine cleavage system is comprised of AMT (known as Protein T), GCSH (known as Protein H), DLD (known as Protein L) and GLDC (known as Protein P), all of which work together to catalyze the cleavage and degradation of glycine. GLDC (glycine dehydrogenase ), also known as GCE, GCSP (glycine cleavage system P protein) or HYGN1, is a 1,020 amino acid protein that localizes to the mitochondria and belongs to the gcvP family. GLDC binds to glycine and enables the methylamine group from glycine to be transferred to the Protein T. GLDC exists as a homodimer and utilizes pyridoxal phosphate as a cofactor. Mutations in the gene encoding GLDC leads to nonketotic hyperglycinemia (NKH), also known as glycine encephalopathy (GCE), an autosomal recessive disease characterized by accumulation of a large amount of glycine in body fluid and by severe neurological symptoms.

Function:
The glycine cleavage system catalyzes the degradation of glycine. The P protein binds the alpha-amino group of glycine through its pyridoxal phosphate cofactor; CO(2) is released and the remaining methylamine moiety is then transferred to the lipoamide cofactor of the H protein.

Subunit:
Homodimer. The glycine cleavage system is composed of four proteins: P, T, L and H.

Subcellular Location:
Mitochondrion.

DISEASE:
Defects in GLDC are a cause of non-ketotic hyperglycinemia (NKH) [MIM:605899]; also known as glycine encephalopathy (GCE). NKH is an autosomal recessive disease characterized by accumulation of a large amount of glycine in body fluid and by severe neurological symptoms.

Similarity:
Belongs to the gcvP family.

Database links:
UniProtKB/Swiss-Prot: P23378.2

Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.kastlife.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 91在线观看 | 精品成人毛片一区二区 | 成人免费视频国一国二在线观看 | 国产亚洲AV夜间福利香蕉149 | chinese45丰满成熟hd | 免费人成视频网站在线18 | 在线看片免费人成视频影院看 | 精品综合久久久久久888蜜芽 | 久久久久久久久一区二区三区 | 欧美日韩一区二 | 一级片性生活 | 韩国日本三级在线 | 久久国产a级久久美女毛片 日韩激情无码一级毛片 | 中文字幕日韩网站免费视频 | 亚洲欧美国产日韩精品 | 婷婷丁香色综合狠狠色 | www.久久视频 | 亚洲AV成人片色在线观看蜜桃 | 免费无码成人AV片在线在线播放 | 国产成人啪精品视频免费网站 | 久久众筹精品私拍模特 | 欧美热久久 | 欧美受xxxx黑人xyx爽 | 久久夜色精品国产噜噜亚洲AV | 国内精品久久久久久久果冻传媒 | 国产草b | 中文字幕一区二区在线视频 | 免费又黄又爽又猛的毛片 | 亚洲欧美国产精品久久久久 | 第一页av | 国产日产欧产精品 | 国产午夜精品久久久久久免费视 | 亚洲精品色播 | 曰韩a级片 | 亚洲精品网站免费 | 国产精品二区三区在线观看 | 成年动漫在线精品视频 | 天天舔天天干天天操 | 午夜三区| 国内在线高清免费视频 | 麻豆传媒一区二区三区 |