97久久久精品综合88久久_亚洲国产精品一_久热热国产久热_97操操操_北条麻妃在线免费观看_精品国自产拍天天拍

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
av片久久,精品伊甸园,天堂新版在线
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-HPS2/Biotin Conjugated antibody (bs-17380R-Bio)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-17380R-Bio
英文名稱 Rabbit Anti-HPS2/Biotin Conjugated antibody
中文名稱 生物素標記的HPS2蛋白抗體
別    名 Adapter related protein complex 3 beta 1 subunit; Adapter-related protein complex 3 subunit beta-1; Adaptor protein complex AP-3 subunit beta-1; Adaptor protein complex AP3 beta1 subunit; ADTB3; ADTB3A; AP-3 complex subunit beta-1; AP3 complex beta1 subunit; AP3B1; AP3B1_HUMAN; Beta-3A-adaptin; Beta3A adaptin; Clathrin assembly protein complex 3 beta 1 large chain; Clathrin assembly protein complex 3 beta-1 large chain; HPS; PE.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 細胞生物  免疫學  信號轉導  轉運蛋白  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 Human, Mouse,  (predicted: Rat, Dog, Pig, Cow, Horse, Rabbit, Sheep, Cat,  Xenopus laevis)
產品應用 WB=1:50-200 ELISA=1:100-1000 IHC-P=1:50-200 IHC-F=1:50-200 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 121kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human HPS2
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
This gene encodes a protein that may play a role in organelle biogenesis associated with melanosomes, platelet dense granules, and lysosomes. The encoded protein is part of the heterotetrameric AP-3 protein complex which interacts with the scaffolding protein clathrin. Mutations in this gene are associated with Hermansky-Pudlak syndrome type 2. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Nov 2012]

Function:
Subunit of non-clathrin- and clathrin-associated adaptor protein complex 3 that plays a role in protein sorting in the late-Golgi/trans-Golgi network (TGN) and/or endosomes. The AP complexes mediate both the recruitment of clathrin to membranes and the recognition of sorting signals within the cytosolic tails of transmembrane cargo molecules. AP-3 appears to be involved in the sorting of a subset of transmembrane proteins targeted to lysosomes and lysosome-related organelles.

Subcellular Location:
Golgi apparatus. Cytoplasmic vesicle > clathrin-coated vesicle membrane. Golgi apparatus. Component of the coat surrounding the cytoplasmic face of coated vesicles located at the Golgi complex.

Tissue Specificity:
Ubiquitously expressed.

Post-translational modifications:
Phosphorylated on serine residues.

DISEASE:
Defects in AP3B1 are the cause of Hermansky-Pudlak syndrome type 2 (HPS2) [MIM:608233]. Hermansky-Pudlak syndrome (HPS) is a genetically heterogeneous, rare, autosomal recessive disorder characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS. HPS2 differs from the other forms of HPS in that it includes immunodeficiency in its phenotype and patients with HPS2 have an increased susceptibility to infections.

Similarity:
Belongs to the adaptor complexes large subunit family.

Database links:

Entrez Gene: 767602 Cow

Entrez Gene: 403459 Dog

Entrez Gene: 8546 Human

Entrez Gene: 11774 Mouse

Entrez Gene: 100049670 Pig

Entrez Gene: 443724 Xenopus laevis

Omim: 603401 Human

SwissProt: Q32PG1 Cow

SwissProt: Q7YRF1 Dog

SwissProt: O00203 Human

SwissProt: Q9Z1T1 Mouse

Unigene: 532091 Human

Unigene: 21185 Mouse



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.kastlife.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 神马午夜窝窝 | 日本aa在线观看 | 无码高潮又爽又黄A片软件 18禁无遮挡免费视频网站 | 成av在线 | 北条麻妃中文字幕 | 日日躁夜夜躁aaaaxxxx | 日本一区二区免费在线播放 | 中文无字幕文字 | 免费黄色在线 | 日韩黄色大片在线观看 | 麻豆www传媒入口 | 亚洲日韩一区精品射精 | 永久免费啪啪的网站入口 | 亚洲中文波霸中文字幕 | 日本羞羞裸色私人影院 | 性视频一区二区三区 | 日日躁夜夜躁人人揉av五月天 | 成人国产三级 | 国产极品美女高潮抽搐免费网站 | 日韩精品免费一区二区三区竹菊 | 日本真人添下面视频免费 | 国产精品白丝jk黑袜喷水视频 | 国产精品一二三区久久狼 | 亚洲国产精品成人久久久 | 国产成人啪精品午夜网站a片免费 | 无码精品人妻一区二区三区老牛 | 少妇太爽了在线观看免费视频 | 中文日产幕无线码一区2023 | 日韩h网站 | 亚洲三区在线观看内射后入 | 久久精品不卡一区二区 | 亚洲不卡在线视频 | 国产高清无码黄片亚洲大尺度视频 | 新版天堂资源中文www官网 | 欧美成人精品A∨在线观看 成人毛片视频在线观看 | 国产在线观看第一页 | 一级全黄男女免费大片 | 人人鲁免费播放视频 | 午夜羞羞影院免费播放在线观看 | 啦啦啦高清在线观看www | 大地资源在线观看免费高清动漫 |