97久久久精品综合88久久_亚洲国产精品一_久热热国产久热_97操操操_北条麻妃在线免费观看_精品国自产拍天天拍

掃碼關(guān)注公眾號(hào)           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
日本欧美在线观看视频,国产精品国产三级囯产AV中文,欧美亚洲精品一区二区
Rabbit Anti-HPS2/BF350 Conjugated antibody (bs-17380R-BF350)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價(jià)
產(chǎn)品編號(hào) bs-17380R-BF350
英文名稱 Rabbit Anti-HPS2/BF350 Conjugated antibody
中文名稱 BF350標(biāo)記的HPS2蛋白抗體
別    名 Adapter related protein complex 3 beta 1 subunit; Adapter-related protein complex 3 subunit beta-1; Adaptor protein complex AP-3 subunit beta-1; Adaptor protein complex AP3 beta1 subunit; ADTB3; ADTB3A; AP-3 complex subunit beta-1; AP3 complex beta1 subunit; AP3B1; AP3B1_HUMAN; Beta-3A-adaptin; Beta3A adaptin; Clathrin assembly protein complex 3 beta 1 large chain; Clathrin assembly protein complex 3 beta-1 large chain; HPS; PE.  
規(guī)格價(jià)格 100ul/2980元 購買        大包裝/詢價(jià)
說 明 書 100ul  
研究領(lǐng)域 細(xì)胞生物  免疫學(xué)  信號(hào)轉(zhuǎn)導(dǎo)  轉(zhuǎn)運(yùn)蛋白  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) Human, Mouse,  (predicted: Rat, Dog, Pig, Cow, Horse, Rabbit, Sheep, Cat,  Xenopus laevis)
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 121kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human HPS2
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene encodes a protein that may play a role in organelle biogenesis associated with melanosomes, platelet dense granules, and lysosomes. The encoded protein is part of the heterotetrameric AP-3 protein complex which interacts with the scaffolding protein clathrin. Mutations in this gene are associated with Hermansky-Pudlak syndrome type 2. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Nov 2012]

Function:
Subunit of non-clathrin- and clathrin-associated adaptor protein complex 3 that plays a role in protein sorting in the late-Golgi/trans-Golgi network (TGN) and/or endosomes. The AP complexes mediate both the recruitment of clathrin to membranes and the recognition of sorting signals within the cytosolic tails of transmembrane cargo molecules. AP-3 appears to be involved in the sorting of a subset of transmembrane proteins targeted to lysosomes and lysosome-related organelles.

Subcellular Location:
Golgi apparatus. Cytoplasmic vesicle > clathrin-coated vesicle membrane. Golgi apparatus. Component of the coat surrounding the cytoplasmic face of coated vesicles located at the Golgi complex.

Tissue Specificity:
Ubiquitously expressed.

Post-translational modifications:
Phosphorylated on serine residues.

DISEASE:
Defects in AP3B1 are the cause of Hermansky-Pudlak syndrome type 2 (HPS2) [MIM:608233]. Hermansky-Pudlak syndrome (HPS) is a genetically heterogeneous, rare, autosomal recessive disorder characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS. HPS2 differs from the other forms of HPS in that it includes immunodeficiency in its phenotype and patients with HPS2 have an increased susceptibility to infections.

Similarity:
Belongs to the adaptor complexes large subunit family.

Database links:

Entrez Gene: 767602 Cow

Entrez Gene: 403459 Dog

Entrez Gene: 8546 Human

Entrez Gene: 11774 Mouse

Entrez Gene: 100049670 Pig

Entrez Gene: 443724 Xenopus laevis

Omim: 603401 Human

SwissProt: Q32PG1 Cow

SwissProt: Q7YRF1 Dog

SwissProt: O00203 Human

SwissProt: Q9Z1T1 Mouse

Unigene: 532091 Human

Unigene: 21185 Mouse



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.kastlife.cn 北京博奧森生物技術(shù)有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號(hào): 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號(hào): CQC24QY10047R0M/1100
京ICP備05066980號(hào)-1         京公網(wǎng)安備110107000727號(hào)
主站蜘蛛池模板: 色噜噜一区二区三区 | 国产被窝福利一区二区 | 久久午夜国产 | 亚洲精品成人三区 | 99在线精品视频观看免费 | 制服丝袜中文字幕无码自拍 | 日本一级片在线观看 | 无码精品人妻免费 | 三区四区乱码不卡 | 国产人妻精品无码AV在线 | 亚洲丰满少妇xxxxx高潮对白 | 久久精品国产精品国产精品污 | 中日字幕大片在线播放 | 亚洲色精品VR一区二区 | 欧美日视频 | 国产成熟女人性满足视频 | 看真人视频一级毛片 | 亚洲精品久久久无码白峰美 | 国产成人AV无码精品天堂 | 国产成人AV片无码免费 | 东京复仇者第三季天竺篇在线观看 | 少妇边打电话边呻吟在线91 | 99精品国产在热久久无毒不卡 | 亚洲网站观看 | 中出乱码av亚洲精品久久天堂 | 日本韩国欧美在线 | 九九热久久免费视频 | 日韩中文字幕手机在线观看 | 人人草人人做人人爱 | 欧美黄色一级 | 国产在线午夜卡精品影院 | 欧美日韩激情在线 | 久久这里精品国产99丫e6 | 性色aⅤ极品无码专区亚洲 成人水多啪啪片 | 天天澡日日澡狠狠欧美老妇 | 亚洲丰满熟妇XXXX性A片 | 成年人视频在线观看免费 | 久久亚洲中文字幕伊人久久大 | 欧美丰满大乳高跟鞋 | 亚洲精品无码久久久久久久 | 99er久久|