97久久久精品综合88久久_亚洲国产精品一_久热热国产久热_97操操操_北条麻妃在线免费观看_精品国自产拍天天拍

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質(zhì)量反饋  關于我們  聯(lián)系我們
冷暖人间第一部,免费看黄色片的网站,长江现货有色金属官网
首頁 > 產(chǎn)品中心 > 標記一抗 > 產(chǎn)品信息
Rabbit Anti-HPS5/Cy5 Conjugated antibody (bs-17383R-Cy5)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產(chǎn)品編號 bs-17383R-Cy5
英文名稱 Rabbit Anti-HPS5/Cy5 Conjugated antibody
中文名稱 Cy5標記的Hermansky-Pudlak綜合征蛋白5抗體
別    名 AIBP63; HPS5_HUMAN; Alpha integrin binding protein 63; Hermansky Pudlak syndrome 5 protein; Ru2; Ruby eye protein 2 homolog.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 細胞生物  信號轉(zhuǎn)導  結(jié)合蛋白  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 Mouse,  (predicted: Human, Rat, Horse, Sheep, )
產(chǎn)品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 127kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human HPS5
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene encodes a protein that may play a role in organelle biogenesis associated with melanosomes, platelet dense granules, and lysosomes. This protein interacts with Hermansky-Pudlak syndrome 6 protein and may interact with the cytoplasmic domain of integrin, alpha-3. Mutations in this gene are associated with Hermansky-Pudlak syndrome type 5. Multiple transcript variants encoding two distinct isoforms have been identified for this gene. [provided by RefSeq, Jul 2008]

Function:
HPS5 may play a role in organelle biogenesis associated with melanosomes, platelet dense granules, and lysosomes. HPS5 interacts with Hermansky-Pudlak syndrome 6 protein and may interact with the cytoplasmic domain of integrin alpha 3. Mutations in HPS5 gene are associated with Hermansky-Pudlak syndrome type 5. Multiple transcript variants encoding two distinct isoforms have been identified for this gene.

Subunit:
Component of the biogenesis of lysosome-related organelles complex-2 (or BLOC2) composed of HPS3, HPS5 and HPS6. Directly interacts with HPS6. May interact with all alpha-integrin chains that have an aromatic residue before the first lysine of the conserved KXGFFKR motif, including ITGA2, ITGA3, ITGA5 and ITGA6.

Subcellular Location:
Cytoplasm, cytosol.

Tissue Specificity:
Widely expressed. Isoform 1:Highly expressed in lungs and testis. Isoform 2:Highly expressed in placenta, kidney, testis ovary, lung and thymus.

DISEASE:
Hermansky-Pudlak syndrome 5 (HPS5) [MIM:614074]: A form of Hermansky-Pudlak syndrome, a genetically heterogeneous autosomal recessive disorder characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS. Note=The disease is caused by mutations affecting the gene represented in this entry.

Similarity:
Belongs to the HPS5 family.

Database links:

Entrez Gene: 11234 Human

Omim: 607521 Human

SwissProt: Q9UPZ3 Human

Unigene: 437599 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.kastlife.cn 北京博奧森生物技術有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
主站蜘蛛池模板: 亚州av久久精品美女模特图片 | 日本乱子人伦在线视频 | 无码纯肉视频在线观看喷水 | 精品人妻中文字幕有码在线 | 国产成人无码a区精油按摩 大地资源在线观看免费高清官网 | 国内视频精品 | 无码人妻精品中文字幕 | 亚洲成人av免费观看 | 日韩精品手机在线 | 毛片a在线 | 日韩精品免费看 | 亚洲国产天堂久久综合网 | 亚洲综合久久一本伊一区 | 亚洲欧美第一成人网站7777 | 偷拍呻吟高潮91 | 亚洲国产日韩在线一区模特 | 久久精品无码AV | 国产成人精品日本亚洲第一区 | 麻豆视频免费 | 好吊操视频 | 国产欧美一区二区三区久久人妖 | 18久久白丝| 一本到不卡免费一区二区 | japan高清日本乱xxxxx | 亚洲免费视频在线观看 | 香蕉久久久久久久AV网站 | 国产在线日韩欧美 | 91视频在线视频 | 日本国产免费 | 伊人逼逼 | 欧美不卡一区 | 色视频网站在线观看 | 视频第一区 | 91看点 | 亚洲最新免费视频 | AV无码岛国免费动作片 | 黄色一区二区三区四区 | 麻豆一区二区大豆行情 | 成人黄色毛片 | 中文字字幕在线乱码 | 中文字幕第25页 |