97久久久精品综合88久久_亚洲国产精品一_久热热国产久热_97操操操_北条麻妃在线免费观看_精品国自产拍天天拍

掃碼關(guān)注公眾號           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
亚洲少妇一区二区,亚洲熟妇无码一区二区三区 ,在线激情视频
Rabbit Anti-Matrilin 3/HRP Conjugated antibody (bs-18694R-HRP)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產(chǎn)品編號 bs-18694R-HRP
英文名稱 Rabbit Anti-Matrilin 3/HRP Conjugated antibody
中文名稱 辣根過氧化物酶標(biāo)記的胞外基質(zhì)蛋白3抗體
別    名 AV009181; DIPOA; EDM5; HOA; MATN3; MATN3_HUMAN; Matrilin 3; Matrilin-3; OADIP; OS2.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領(lǐng)域 細(xì)胞生物  發(fā)育生物學(xué)  信號轉(zhuǎn)導(dǎo)  細(xì)胞外基質(zhì)  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) (predicted: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Rabbit, Guinea Pig, Cat, )
產(chǎn)品應(yīng)用 WB=1:500-2000 ELISA=1:100-1000 IHC-P=1:50-200 IHC-F=1:50-200 ICC=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 53kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human Matrilin 3
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene encodes a member of von Willebrand factor A domain containing protein family. This family of proteins is thought to be involved in the formation of filamentous networks in the extracellular matrices of various tissues. This protein contains two von Willebrand factor A domains; it is present in the cartilage extracellular matrix and has a role in the development and homeostasis of cartilage and bone. Mutations in this gene result in multiple epiphyseal dysplasia. [provided by RefSeq, Jul 2008]

Function:
Major component of the extracellular matrix of cartilage and may play a role in the formation of extracellular filamentous networks.

Subcellular Location:
Secreted.

Tissue Specificity:
Expressed only in cartilaginous tissues, such as vertebrae, ribs and shoulders.

DISEASE:
Defects in MATN3 are the cause of multiple epiphyseal dysplasia type 5 (EDM5) [MIM:607078]. EDM is a generalized skeletal dysplasia associated with significant morbidity. Joint pain, joint deformity, waddling gait, and short stature are the main clinical signs and symptoms. EDM is broadly categorized into the more severe Fairbank and the milder Ribbing types. EDM5 is relatively mild and clinically variable. It is primarily characterized by delayed and irregular ossification of the epiphyses and early-onset osteoarthritis.
Defects in MATN3 are the cause of spondyloepimetaphyseal dysplasia MATN3-related (SEMD-MATN3) [MIM:608728]. A bone disease characterized by disproportionate early-onset dwarfism, bowing of the lower limbs, lumbar lordosis and normal hands. Skeletal abnormalities include short, wide and stocky long bones with severe epiphyseal and metaphyseal changes, hypoplastic iliac bones and flat, ovoid vertebral bodies.
Genetic variations in MATN3 are associated with susceptibility to osteoarthritis type 2 (OS2) [MIM:140600]; also called osteoarthritis of distal interphalangeal joints (OADIP) or hand osteoarthritis (HOA). Osteoarthritis is a degenerative disease of the joints characterized by degradation of the hyaline articular cartilage and remodeling of the subchondral bone with sclerosis. Clinical symptoms include pain and joint stiffness often leading to significant disability and joint replacement. In the hand, osteoarthritis can develop in the distal interphalangeal and the first carpometacarpal (base of thumb) and proximal interphalangeal joints. Patients with osteoarthritis may have one, a few, or all of these sites affected.

Similarity:
Contains 4 EGF-like domains.
Contains 1 VWFA domain.

Database links:

Entrez Gene: 4148 Human

Entrez Gene: 17182 Mouse

Entrez Gene: 313954 Rat

Omim: 602109 Human

SwissProt: O15232 Human

SwissProt: O35701 Mouse

Unigene: 656199 Human

Unigene: 42226 Mouse



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.kastlife.cn 北京博奧森生物技術(shù)有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
主站蜘蛛池模板: 午煮香蕉小辣椒 | 中文字幕1区2区 | 欧美日视频 | 一本之道中文日本高清 | 国产女人50精品二区毛片视涩漫 | 国产实拍会所女技师在线观看 | 免费人成视频在线观看播放网站 | 一级特黄毛片 | 中文字幕日本 | 国产在线第一区 | 极品白嫩粉嫩美女国产 | 色花堂国产精品第一页 | 无码精品国产DVD在线观看9久 | 国产精品成人av | 国产日韩AV免费无码一区二区三区 | 色欲精品国产一区二区三区AV | 久久不见久久见中文字幕免费 | 在线观看三级网站 | a级片黄 | 强插女教师AV在线 | 成人欧美一区二区三区小说 | 超碰91青青国产福利手机看片 | 曰本A级毛片无卡免费视频 久久热这里只有精品在线观看 | 成人影院亚洲 | 尤物丰满少妇大尺度喷血写真 | 国产网红主播精品一区二区三区 | 国产成人精品怡红院在线观看 | 欧美变态口味重另类在线视频 | 18videossex性欧美69| 青青操五月天 | 欧美xvideosexo另类 | 欧美高清69 | 清纯唯美经典一区二区 | 色婷婷五月综合丁香中文字幕 | 久久久久亚洲AV无码网站 | 一个人看的www视频免费播放 | 91桃色在线 | 色婷婷av一区二区三区软件 | 提莫影院AV毛片入口 | 国产午夜精品免费一区二区三区 | 公和我做好爽添在厨房 |