97久久久精品综合88久久_亚洲国产精品一_久热热国产久热_97操操操_北条麻妃在线免费观看_精品国自产拍天天拍

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
国产亚洲另类久久久精品,久久人人97超碰精品888,www.色香蕉
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-PLOD3/Cy5 Conjugated antibody (bs-12732R-Cy5)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-12732R-Cy5
英文名稱 Rabbit Anti-PLOD3/Cy5 Conjugated antibody
中文名稱 Cy5標記的賴氨酸羥化酶3抗體
別    名 2-oxoglutarate 5-dioxygenase 3; bone protein I; BP-I; LH3; Lysine hydroxylase 3; Lysyl hydroxylase 3; Plod3; PLOD3_HUMAN; Procollagen lysine,2 oxoglutarate 5 dioxygenase 3 precursor; Procollagen-lysine.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 細胞生物  免疫學  細胞膜蛋白  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 Mouse,  (predicted: Human, Rat, Dog, Pig, Cow, Horse, Rabbit, Sheep, )
產品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 82kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human PLOD3
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
The protein encoded by this gene is a membrane-bound homodimeric enzyme that is localized to the cisternae of the rough endoplasmic reticulum. The enzyme (cofactors iron and ascorbate) catalyzes the hydroxylation of lysyl residues in collagen-like peptides. The resultant hydroxylysyl groups are attachment sites for carbohydrates in collagen and thus are critical for the stability of intermolecular crosslinks. Some patients with Ehlers-Danlos syndrome type VIB have deficiencies in lysyl hydroxylase activity. [provided by RefSeq, Jul 2008]

Function:
Forms hydroxylysine residues in -Xaa-Lys-Gly- sequences in collagens. These hydroxylysines serve as sites of attachment for carbohydrate units and are essential for the stability of the intermolecular collagen cross-links.

Subcellular Location:
Rough endoplasmic reticulum membrane.

DISEASE:
Defects in PLOD3 are the cause of lysyl hydroxylase 3 deficiency (LH3 deficiency) [MIM:612394]; also known as bone fragility with contractures arterial rupture and deafness. LH3 deficiency is a connective tissue disorder. The syndrome is characterized by congenital malformations severely affecting many tissues and organs and revealing features of several collagen disorders, most of them involving COL2A1 (type II collagen). The findings suggest that the failure of lysyl hydroxylation and hydroxylysyl carbohydrate addition, which affects many collagens, is the molecular basis of this syndrome.

Similarity:
Contains 1 Fe2OG dioxygenase domain.

Database links:

Entrez Gene: 8985 Human

Entrez Gene: 26433 Mouse

Entrez Gene: 288583 Rat

Omim: 603066 Human

SwissProt: O60568 Human

SwissProt: Q9R0E1 Mouse

SwissProt: Q5U367 Rat

Unigene: 153357 Human

Unigene: 251003 Mouse

Unigene: 90152 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.kastlife.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 久久国产亚洲日韩 | 日韩精品一区二区三区免费观看 | 黄色大全免费观看 | 91视频九色欧美 | 国产精品一区二区三区视频网站 | 一级免费看片 | 久久亚洲中文字幕伊人久久大 | 欧美性受xxxx | 篱笆女人狗电视连续剧第一部 | 国产女同一区二区在线 | 欧美视频国产 | 久久一精品 | 御姐av在线 | 999国产在线 | 超碰在线98 | 国产V亚洲V天堂A无码 | 国产欧美一区二区三区国产幕精品 | 久久曰曰 | 日韩精品国产自在久久现线拍 | 男人天堂亚洲成人 | 日日天干夜夜人人添 | 99视频在线无码 | 观看av| 中文字幕乱码亚洲无线码 | 欧美日韩不卡一区二区 | 国产一级特黄高清在线大片 | 亚洲中文成人中文字幕 | 久久久久久国产精品免费无遮挡 | 91免费高清观看 | 亚洲a在线播放 | 婷婷久久国产对白刺激五月99 | 欧美日韩高清一区二区三区 | japanese乱人伦精品 | 精品人妻一区二区三区四区在线 | 女人爽到高潮免费视频大全 | 欧美国产成人精品二区芒果视频 | 日韩免费视频播放 | 国产美女精品福利一区二区 | 少妇对白露脸打电话系列 | 美女扒开腿让男人桶爽网站 | 狼人无码中文在线观看 |